Ectodermal dysplasia (ED) comprises a group of rare inherited disorders characterized by abnormal development of ectodermal structures such as skin, hair, nails, teeth, and sweat glands. This paper provides an overview of major ED subtypes, including hypohidrotic, hidrotic, and other syndromic forms, highlighting their genetic etiology, clinical manifestations, and particularly the significant dental anomalies they cause. The report emphasizes the importance of early diagnosis and multidisciplinary management, especially concerning dental rehabilitation. A detailed case report of a 14-year-old boy with hypohidrotic ectodermal dysplasia illustrates the clinical challenges and prosthodontic management strategies involved. The patient, presenting with severe oligodontia and facial anomalies, was rehabilitated with custom complete dentures tailored for psychological and functional improvement. The discussion underscores the critical role of prosthetic interventions in maintaining aesthetics, mastication, and speech, while accommodating growth. The article concludes by advocating for timely prosthodontic care and individualized treatment planning, paving the way for future implant-supported solutions post-skeletal maturity.
Keywords: Ectodermal dysplasia, Clinical manifestation, Management
